Schneiderman Prelims Vol-I. qxd

PARANEOPLASTIC DISORDERS
Bazex syndrome (acrokeratosis paraneoplastica) 
AD
141:389–394, 2005
PHOTODERMATOSES
Actinic prurigo
Chronic actinic damage
Chronic actinic dermatitis
Polymorphic light eruption
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A CLINICIAN’S GUIDE TO DERMATOLOGIC DIFFERENTIAL DIAGNOSIS, VOLUME 1
Schneiderman page 500-600.qxd 5/16/2006 6:51 PM Page 572

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PRIMARY CUTANEOUS DISEASES
Acne vulgaris
Acne rosacea, including granulomatous rosacea – indurated red
nose 
JAAD 38:310–313, 1998
Granuloma faciale
Granulosis rubra nasi 
Ann DV 123:106–108, 1996; G Ital DV
125:275–276, 1990; Derm Z 71:79–84, 1935
Lichen simplex chronicus
Perioral dermatitis
Psoriasis
Rhinophyma – indurated red nose 
JAAD 38:310–313, 1998
Seborrheic dermatitis
SYNDROMES
Amyoplasia congenita disruptive sequence – mid-facial macular
telangiectatic nevi 
Am J Med Genet 15:571–590, 1983
Beckwith–Wiedemann syndrome (exomphalos–macroglossia–
gigantism) (EMG) syndrome – autosomal dominant; zosteriform
rash at birth, exomphalos, macroglossia, visceromegaly, facial
salmon patch of forehead, upper eyelids, nose, and upper lip
and gigantism; linear earlobe grooves, circular depressions
of helices; increased risk of Wilms’ tumor, adrenal carcinoma,
hepatoblastoma, and rhabdomyosarcoma 
JAAD 37:523–549,
1997; Am J Dis Child 122:515–519, 1971
Bloom’s syndrome
Bonnet–Dechaume–Blanc syndrome – midfacial arteriovenous
malformation 
Textbook of Neonatal Dermatology, p.329, 2001
Cornelia de Lange syndrome – specific facies, hypertrichosis of
forehead, face, back, shoulders, and extremities, synophrys;
long delicate eyelashes, cutis marmorata, skin around eyes
and nose with bluish tinge, red nose 
Ped Derm 19:42–45, 2002;
Rook p.428, 1998, Sixth Edition; JAAD 37:295–297, 1997
Lethal multiple pterygium syndrome – mid-facial macular
telangiectatic nevi 
Am J Med Genet 12:377–409, 1982
Lipoid proteinosis 
Ped Derm 9:264–267, 1992
Multicentric reticulohistiocytosis
Robert’s syndrome (hypomelia–hypotrichosis–facial
hemangioma syndrome) – autosomal recessive; mid-facial
port wine stain extending from forehead to nose and philtrum,
cleft lip 
+
/
−
cleft palate, sparse silver-blond hair, limb reduction
malformation, characteristic facies, malformed ears with
hypoplastic lobules, marked growth retardation 
Clin Genet
5:1–16, 1974; Clin Genet 31:170–177, 1987
Sjögren’s syndrome – erythema of nose and cheeks 
Rook
p.2572, 1998, Sixth Edition
Sphenopalatine syndrome – chronic and intermittent edema of
face with unilateral lacrimation, rhinitis, erythema of the bridge
of the nose 
Rook p.2782, 1998, Sixth Edition
Trichorhinophalangeal syndrome (bulbous nose) 
Ped Derm
10:385–387, 1993
Tuberous sclerosis – adenoma sebaceum 
Plast Reconstruct
Surg 70:91–93, 1981