Schneiderman Prelims Vol-I. qxd

BUTTERFLY RASH
109
Schneiderman page 100-200.qxd 5/16/2006 6:49 PM Page 109

---

Atopic dermatitis
Darier’s disease
Epidermolysis bullosa, junctional lethal type (atrophicans
generalisata gravis, Herlitz type) – extensive blistering and
erosions at birth; perioral and nasal exuberant granulation
tissue in butterfly distribution 
Rook p.1828–1829, 1998, Sixth
Edition; Epidermolysis Bullosa: Basic and Clinical Aspects.
New York: Springer, 1992:118–134
Erythromelanosis follicularis faciei 
JAAD 32:863–866, 1995
Erythrosis pigmentata faciei (erythrose peribuccale pigmentaire
of Brocq) 
Ghatan p.60,253, 2002, Second Edition
Granuloma faciale
Granulosis rubra nasi
Impetigo herpetiformis
Keratosis pilaris
Lentiginosis – acquired generalized
Ofuji’s disease – eosinophilic pustular folliculitis
Perioral dermatitis
Pityriasis rosea
Pityriasis rubra pilaris
Psoriasis
Seborrheic dermatitis, including AIDS-associated seborrheic
dermatitis 
BJD 111:603–607, 1984
Ulerythema ophyrogenes
Vitiligo
PSYCHOCUTANEOUS
Factitial dermatitis
SYNDROMES
Ataxia telangiectasia – telangiectasias in butterfly distribution,
of bulbar conjunctivae, tip of nose, ears, antecubital and popliteal
fossae, dorsal hands and feet; atrophy with mottled hypo- and
hyperpigmentation, dermatomal CALMs, photosensitivity,
canities, acanthosis nigricans, dermatitis; cutaneous granulomas
present as papules or nodules, red plaques with atrophy or
ulceration 
Rook p.2095,1998, Sixth Edition; JAAD 10:431–438,
1984; Ann Intern Med 99:367–379, 1983
Bazex syndrome (acrokeratosis paraneoplastica) 
Bloom’s syndrome (congenital telangiectatic erythema and
stunted growth) – autosomal recessive; slender face, prominent
nose; facial telangiectatic erythema with involvement of eyelids,
ear, hand and forearms; bulbar conjunctival telangiectasias;
stunted growth; CALMs, clinodactyly, syndactyly, congenital
heart disease, annular pancreas, high-pitched voice, testicular
atrophy; no neurologic deficits 
Ped Derm 22:147–150, 2005;
Ped Derm 14:120–124, 1997; JAAD 17:479–488, 1987; Am J
Hum Genet 21:196–227, 1969; AD 94:687–694, 1966; Am J
Dis Child 88:754–758, 1954
Carcinoid syndrome – foregut (stomach, lung, pancreas) –
bright red geographic flush, sustained, with burning, lacrimation,
wheezing, sweating; hindgut (ileal) – patchy, violaceous,
intermixed with pallor, short duration 
Rook p.2101, 1998,
Sixth Edition; edema, telangiectasia, cyanotic nose and face,
rosacea 
Acta DV (Stockh) 41:264–276, 1961; white macules
surrounded by erythema and telangiectasia 
BJD 90:547–551,
1974; pellagrous lesions Am Heart J 47:795–817, 1954
Cockayne syndrome – autosomal recessive; xerosis with
rough, dry skin, anhidrosis, erythema of hands, hypogonadism;
short stature, facial erythema in butterfly distribution leading
to mottled pigmentation and atrophic scars, premature aged
appearance with loss of subcutaneous fat and sunken eyes,
canities, mental deficiency, photosensitivity, disproportionately
large hands, feet, and ears, ocular defects, demyelination 
Ped
Derm 20:538–540, 2003; Am J Hum Genet 50:677–689, 1992;
J Med Genet 18:288–293, 1981
Dubowitz’s syndrome
Haber’s syndrome – rosacea-like facial erythema
Hartnup’s disease
Reiter’s syndrome
Reticular erythematous mucinosis syndrome (REM syndrome) 
Rothmund–Thomson syndrome (poikiloderma congenitale) –
autosomal recessive 
Am J Med Genet 22:102:11–17, 2001;
Ped Derm 18:210–212, 2001; Ped Derm 16:59–61, 1999;
Dermatol Clin 13:143–150, 1995; JAAD 27:75–762, 1992
Sjögren’s syndrome – erythema of nose and cheeks
Rook p.2572, 1998, Sixth Edition
Sweet’s syndrome
Touraine centrofacial lentiginosis
Tuberous sclerosis
TOXINS
Mercury poisoning – butterfly rash, flushing, perspiration of face,
palmar erythema 
JAAD 45:966–967, 2001
Scombroid fish poisoning – facial flush