NEOPLASTIC
Aortic tumors – aortic angiosarcoma with cutaneous
metastases
JAAD 43:930–933, 2000; primary aortic tumors
Oncology 39:167–172, 1982
Atrial myxoma
BJD 147:379–382, 2002; Cutis 62:275–280,
1998; JAAD 32:881–883, 1995; JAAD 25:110–111, 1991
Gamma heavy chain disease
JAAD 23:988–991, 1990
Inflammatory breast carcinoma
JAAD 52:1009–1019, 2005
Leukemia – chronic myelogenous leukemia with leukostasis;
acral livedo
AD 123:921–924, 1987; acute lymphocytic leukemia
JAAD 52:1009–1019, 2005
Lymphomas – cutaneous T-cell lymphoma
JAAD 52:1009–1019,
2005; intravascular large cell lymphoma JAAD 39:318–321, 1998
Multiple myeloma with paraproteins and crystaloglobulins
JAAD 52:1009–1019, 2005
Livedo reticularis, primary
JAAD 52:1009–1019, 2005
Nevus oligemicus
AD 117:111–113, 1981
Pheochromocytoma
JAAD 52:1009–1019, 2005
Polycythemia vera
JAAD 26:264–265, 1992
Renal cell carcinoma
JAAD 52:1009–1019, 2005
Essential thrombocythemia
JAAD 24:59–63, 1991; Br J
Haematol 36:553–564, 1977; AD 87:302–305, 1963
Waldenström’s macroglobulinemia
AD 134:1127–1131, 1998;
cryoglobulin-associated livedo reticularis
JAAD 45:S202–206, 2001
NORMAL
Cutis marmorata – physiologic
JAAD 52:1009–1019, 2005
Physiologic
PHOTODERMATOSES
Livedo reticularis, photosensitive
AD 108:100–101, 1973
PRIMARY CUTANEOUS DISEASES
Lichen planus
Rook p.966, 1998, Sixth Edition
Livedo reticularis, primary
JAAD 52:1009–1019, 2005
Nevus anemicus
Psoriasis
Cutis 39:429–432, 1987
Symmetrical lividity of the soles
BJD 37:123–125, 1925
SYNDROMES
Adams–Oliver syndrome – aplasia cutis congenita,
cutis marmorata telangiectatica congenital, transverse
limb defects
Ped Derm 22:206–209, 2005
Antiphospholipid antibody syndrome
NEJM 346:752–763,
2002; Semin Arthritis Rheum 31:127–132, 2001; JAAD
36:149–168, 1997; JAAD 36:970–982, 1997; BJD
120:419–429, 1989; IgG-1 antibodies to
β
2
-glycoprotein 1
Am J Med 101:472–281, 1996
Carcinoid syndrome
JAAD 52:1009–1019, 2005
Cardio-facio-cutaneous syndrome
Cornelia de Lange (Brachmann–de Lange) syndrome –
generalized hypertrichosis, confluent eyebrows, low hairline,
hairy forehead and ears, hair whorls of trunk, cutis marmorata,
single palmar crease, physical and mental retardation
JAAD 52:1009–1019, 2005; Am J Med Genet 47:959–964,
1993; marbling around the eyes and nose
Corticomeningeal angiomatosis
Eur Neurol 9:202–215, 1973
Down’s syndrome
JAAD 52:1009–1019, 2005
Macrocephaly cutis marmorata syndrome – hemangioma of
philtrum of upper lip, syndactyly of toes, hyperelastic skin
capillary and cavernous hemangiomas
Clin Dysmorphol
6:291–302, 1997
Neurofibromatosis – vasculopathy
JAAD 51:656–659, 2004;
neurofibromatosis type I – plexiform neurofibroma with
pressure-induced arterial occlusion and livedo racemosa
JAAD 50:S107–109, 2004
Nicolau syndrome – following intramuscular injection
(of bismuth, diclofenac, ibuprofen), intra-arterial, acute
ischemia, severe pain, livedo, necrosis of skin and muscle,
dendritic extension, ulcer, necrotic eschar, atrophic scar
BJD 150:385–387, 2004; J Eur Acad Dermatol 15:585–588,
2001; Ped Derm 12:187–190, 1995; Ann Intern Med
117:1058, 1992
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