Schneiderman Prelims Vol-I. qxd

INFILTRATIVE DISEASES
Amyloidosis – primary systemic;
β
2
-microglobulin amyloidosis –
shoulder pain, carpal tunnel syndrome, flexor tendon deposits
of hands, lichenoid papules, hyperpigmentation, subcutaneous
nodules (amyloidomas) 
Int J Exp Clin Inves 4:187–211, 1997
Mastocytosis – arthralgias 
Ghatan p.171, 2002, Second Edition
Scleromyxedema 
Dermatol Clin 20:493–501, 2002; JAAD
33:37–43, 1995; linear papules, leonine facies, arthritis and
rash, sclerodermoid changes 
JAAD 44:273–281, 2001
Self-healing (papular) juvenile cutaneous mucinosis –
arthralgias 
JAAD 50:S97–100, 2004; JAAD 44:273–281, 2001;
Ped Derm 20:35–39, 2003; Ped Derm 14:460–462, 1997; AD
131:459–461, 1995; JAAD 11:327–332, 1984; Ann DV
107:51–57, 1980
Acute onset, polyarthritis, young age; rapid spontaneous
resolution
Non-tender ivory white papules of the head, neck, trunk;
periarticular
Deep nodules on face and periarticular regions
Hard periorbital edema, cheek bone areas
INFLAMMATORY DISEASES
Angioimmunoblastic lymphadenopathy – polyarthritis, rash, and
lymphadenopathy 
Clin Rheumatol 17:148–151, 1998
Aphthous stomatitis, recurrent 
Clin Exper Rheumatol
14:407–412, 1996
Eosinophilic fasciitis – symmetric polyarthritis 
JAAD
49:1170–1174, 2003; AD 131:1329–1334, 1995
Erythema multiforme, Stevens-Johnson syndrome –
polyarthritis 
Rook p.2084, 1998, Sixth Edition
Erythema nodosum 
Rook p.2200, 1998, Sixth Edition;
Ann Rheum Dis 19:174–180, 1960; Lofgren’s syndrome –
erythema nodosum with sarcoidosis and arthralgias 
Ped Derm
22:366–368, 2005
Hidradenitis suppurativa spondyloarthropathy
Interstitial granulomatous dermatitis with plaques (aka linear
rheumatoid nodule, railway track dermatitis, linear granuloma
annulare) – red, linear plaques with arthritis
JAAD 46:892–899, 2002; linear erythematous cords
JAAD 45:286–291, 2001; JAAD 34:957–961, 1996
Pruritic linear urticarial rash, fever, and systemic inflammatory
disease of adolescents – urticaria, linear lesions, periorbital
edema and erythema, and arthralgia 
Ped Derm 21:580–588,
2004
Pyoderma gangrenosum – association with rheumatoid arthritis,
Behçet’s disease with polyarthritis 
Rook p.2188, 1998,
Sixth Edition; inflammatory bowel disaese AD 125:57–64, 1989;
pyoderma gangrenosum, palmoplantar pustulosis, and chronic
recurrent multifocal osteomyelitis 
Ped Derm 15:435–438, 1998
SAPHO syndrome (pustulosis palmaris plantaris with
arthrosteitis) (sternoclavicular osteitis and palmoplantar
pustulosis) 
AD 128:699–700, 1992; JAAD 18:666–671, 1988
Sarcoid 
AD 111:362, 1975 Clinics in Chest Medicine
18:663–679, 1997; AD 133:882–888, 1997; NEJM
336:1224–1234, 1997
Papules
Eyelids, alae nasi
Bright red, blue red, brown
Annular, lichenoid
Maculopapular
Nodules
Subcutaneous (Darier-Roussy) 
Am J Med 85:731–736, 1988
Plaques
Lupus pernio
Destructive, disfiguring
Violaceous
‘Turkey ears’
Associated with chronic progressive fibrotic pulmonary
disease, upper respiratory mucosal disease, bone cysts of
the fingers, fusiform swelling of the digits; nasal ulceration,
septal perforation
Verrucous papillomatous