VASCULAR
Arteriosclerosis
Rook p.964,2229, 1998, Sixth Edition
Atrophie blanche – livedo with summer (winter) ulcerations
JAAD 8:792–798, 1983; AD 119:963–969, 1983
Cholesterol emboli
BJD 146:1107–1108, 2002;
BJD 146:511–517, 2002; BJD 146:511–517, 2002;
Rook p.2229, 1998, Sixth Edition; Medicine 74:350–358,
1995; Angiology 38:769–784, 1987; AD 112:1194–1198,
1986; JAAD 13:235–242, 1985
Churg–Strauss disease
Medicine 78:26–37, 1999;
JAAD 37:199–203, 1997; BJD 127:199–204, 1992
Coarctation of the aorta – cutaneous mottling of arm
BJD 148:1066–1068, 2003
Congestive heart failure – stasis
Down’s syndrome
Rook p.373, 1998, Sixth Edition
Factor XII deficiency – livedo with ulceration
BJD 143:897–899,
2000
Fat emboli
JAAD 52:1009–1019, 2005
Hypertensive ulcer (Martorell’s ulcer) – very painful ulcer of lower
lateral leg with livedo at edges
Phlebology 3:139–142, 1988
Intramural thrombus – embolus
Klippel–Trenaunay–Weber syndrome
Livedo racemosa
Livedo reticularis – acquired idiopathic
Livedo reticularis with winter ulceration
Malignant angioendotheliomatosis (angiocentic lymphoma) –
scalp; livedoid red plaque of thigh with woody induration
Rook
p.2396, 1998, Sixth Edition; JAAD 18:407–412, 1988
Moyamoya disease – narrowing or occlusion of supraclinoid
portion of the internal carotid artery and stems of anterior and
middle cerebral arteries
Ped Derm 20:124–127, 2003
Neurologic syndromes – cerebral vascular accidents, transient
ischemic attacks
Parkes–Weber syndrome
Peripheral vascular disease
Vessel wall disease – arteriosclerotic, hyperparathyroidism,
arteritis (PAN, rheumatoid arthritis, LE, dermatomyositis,
lymphoma, syphilis, tuberculosis, pancreatitis)
JAAD18:1003–1019, 1988
Port wine stain (nevus flammeus) with reticulate pattern
Primary pulmonary hypertension
Raynaud’s disease and phenomenon
Sturge–Weber syndrome
Symmetric peripheral gangrene
Thromboangiitis obliterans (Buerger’s disease)
Rook p.2233,
1998, Sixth Edition; Am J Med Sci 136:567–580, 1908
Tumor emboli
Vascular malformation with overlying slow flow
Vasculitis
(adopted from Current Prob Derm, Vol V, No.2, 1993)
Small vessel vasculitis
Circulating immune complexes
Collagen vascular disease – SLE, rheumatoid arthritis,
dermatomyositis, Sjögren’s syndrome, scleroderma
Cutis
39:429–432, 1987
Drug-induced vasculitis
Erythema elevatum diutinum
Familial Mediterranean fever
Henoch–Schönlein purpura; HSP of adults
AD 125:53–56,
1989
Livedoid vasculitis – livedo with summer ulcerations
JAAD 51:574–579, 2004
Mixed cryoglobulinemia
Organ transplant vasculitis
Paraneoplastic vasculitis
Serum sickness
Transplacental transient vasculitis
JAAD 52:1009–1019, 2005
Vasculitis of C2 deficiency
Vasculitis associated with cystic fibrosis
Vasculitis associated with subacute bacterial endocarditis
Small vessel lymphocytic vasculitis with winter or summer
ulcerations
Small and medium-sized vessel vasculitis
Churg–Strauss granulomatosis
JAAD 47:209–216, 2002
Dermatomyositis
Lupus erythematosus
Lymphomatoid granulomatosis
Lymphomas
Microscopic polyangiitis
JAAD 52:1009–1019, 2005
Necrotizing sarcoid granulomatosis
Nodular vasculitis
JAAD 52:1009–1019, 2005
Pancreatitis
Polyarteritis nodosa (PAN) – nodules along the course of
superficial arteries around knee, anterior lower leg and
dorsum of foot
JAAD 53:724–728; JAAD 48:311–340,
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