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[Encyclopedia of Differential Diagnosis in Dermatology] Paul Schneiderman, Marc E. Grossman - A Clinician\'s Guide to Dermatologic Differential Diagnosis, Volume 1 The Text (Encyclopedia of Differential Diagnosis in D

PARANEOPLASTIC
Acanthosis nigricans 
BJD 153:667–668, 2005
Paraneoplastic annular erythema – perigenital dermatitis
PRIMARY CUTANEOUS DISEASE
Acantholytic dermatosis of the vulvo-crural area – vulvar
papules, cobblestoning of the vulva and thighs 
Cutis
67:217–219, 2001; Am J Dermatopathol 6:557–560, 1984
Acanthosis nigricans – velvety plaques, intertriginous
pigmentation 
Rook p.1583–1585,3168, 1998, Sixth Edition
294
A CLINICIAN’S GUIDE TO DERMATOLOGIC DIFFERENTIAL DIAGNOSIS, VOLUME 1
Schneiderman page 200-300.qxd 5/16/2006 6:49 PM Page 294


Atopic dermatitis
Confluent and reticulated papillomatosis – velvety plaques,
intertrigenous pigmentation
Cutis laxa
Darier’s disease – autosomal dominant; intertriginous
pigmentation; photo-aggravated in seborrheic distribution;
skin-colored, brown, yellow–brown papules which may coalesce
into verrucous plaques or papillomatous masses; acrokeratosis
verruciformis of Hopf, palmar and plantar pits, cobblestoned
mucous membranes
Dermatospiraxis in children – groin fissures 
AD 129:131–1315,
1993
Diaper dermatitis with rapid dissemination – expanding
nummular dermatitis of trunk, and red scaly plaques of neck
and axillae (‘psoriasiform id’) 
BJD 78:289–296, 1966
Dowling–Degos disease – velvety plaques and intertriginous
pigmentation 
AD 114:1150–1157, 1978; AD 114:1150–1157,
1976
Eccrine squamous syringometaplasia – red plaques in axillae
and groin 
AD 133:873–878, 1997
Elastosis perforans serpiginosa with pseudoxanthoma
elasticum-like changes in Moya–Moya disease (bilateral
stenosis and occlusion of basa intracranial vessels and carotid
arteries) 
BJD 153:431–434, 2005
Epidermolysis bullosa atrophicans inversa (dermolytic
dystrophic) 
Epidermolysis bullosa inversa – early generalized involvement
with blisters and erosions healing with superficial atrophic scars
persisting into adulthood; blisters of trunk, proximal extremities,
including the axillae, groin and perineum; form of junctional
epidermolysis bullosa with oral blisters, dysplastic teeth,
dystrophic toenails with normal fingernails, hoarseness, corneal
erosions and albostriate lesions 
JAAD 12:836–844, 1985;
AD 124:544–547, 1988
Epidermolysis bullosa – junctional epidermolysis bullosa, Herlitz
type – erosive diaper dermatitis 
Ped Derm 14:307–311, 1997
Erythema annulare centrifugum
Erythema of Jacquet – erosive diaper dermatitis; shallow, round
ulcers with raised edges; umbilicated papules, erosions 
Ped
Derm 15:46–47, 1998; Rook p.470, 1998, Sixth Edition
Erythrokeratoderma variabilis
Fox–Fordyce disease
Galli–Galli syndrome – Dowling–Degos disease with
acantholysis – hyperkeratotic follicular papules 
JAAD
45:760–763, 2001
Granular parakeratosis – hyperkeratotic papules and plaques
in the intertriginous areas in children (infantile granular
parakeratosis) 
JAAD 52:863–867, 2005; JAAD 50S93–96,
2004; BJD 147:1003–1006, 2002; Ped Derm 19:146–147, 2002;
axillary (or submammary) granular hyperkeratosis (axillary
granular parakeratosis) – unilateral or bilateral pruritic
erythematous or hyperpigmented patches; punctate
hyperkeratosis; keratohyaline granules are retained in the
markedly thickened stratum corneum
AD 140:1161–1166, 2004; JAAD 47:S279–280, 2002;
AD 137:1241–1246, 2001; JAAD 40:813–814, 1999;
JAAD 39:495–496, 1998; JAAD 37:789–790, 1997;
JAAD 33:373–375, 1995; JAAD 24:541–544, 1991
Greither’s palmoplantar keratoderma – linear axillary
hyperkeratosis; hyperkeratosis of elbows, knees, shins J
AAD
53:S225–230, 2005
Hailey–Hailey disease 
BJD 126:275–282, 1992; Arch Dermatol
Syphilol 39:679–685, 1939
Impetigo herpetiformis (pustular psoriasis of pregnancy) –
symmetrical and grouped lesions, starting in flexures
(inguinocrural areas) 
AD 136:1055–1060, 2000; AD 127:91–95,
1996; Acta Obstet Gynecol Scand 74:229–232, 1995
Interstitial granulomatous dermatitis – axillary folds and groin;
may be drug-induced 
BJD 150:1035–1037, 2004
Kitamura’s disease – intertriginous pigmentation
Leiner’s disease
Lichen planus 
Rook p.3167, 1998, Sixth Edition
Lichen sclerosus et atrophicus 
Rook p.2549–2551, 1998,
Sixth Edition; axillary Cutis 69:285–287, 2002
Lichen simplex chronicus 
Rook p.3168, 1998, Sixth Edition
Lupus miliaris disseminatus faciei (acne agminata) – axillary
Clin Exp Dermatol 23:125–128, 1998
Miliaria rubra in infants – red papular eruption of neck, axilla,
groin 
BJD 99:117–137, 1978
Non-bullous CIE (congenital ichthyosiform erythroderma)
(erythrodermic lamellar ichthyosis) – autosomal recessive –
intertrigo-like pattern 
Rook p.1497, 1998, Sixth Edition;
AD 121:477–488, 1985
Pityriasis rosea
Poikiloderma vasculare atrophicans
Progressive symmetric erythrokeratoderma – intertriginous
and perigenital; must be differentiated from erythrokeratoderma
variabilis (migrating erythematous patches) and localized forms
of pityriasis rubra pilaris 
AD 122:434–440, 1986
Psoriasis, including napkin psoriasis 
Textbook of Neonatal
Dermatology, p.249, 2001; Rook p.1602, 1998, Sixth Edition;
Contact Dermatitis 26:248–252, 1992; BJD 773:445–447, 1961
Pyoderma vegetans 
AD 116:1169–1171, 1980
Seborrheic dermatitis 
Rook p.3167, 1998, Sixth Edition
Subcorneal pustular dermatosis of Sneddon–Wilkinson –
pustules which expand to annular and serpiginous lesions
with scaly edge; heal with hyperpigmentation 
Ped Derm
20:57–59, 2003; BJD 145:852–854, 2001; J Dermatol
27:669–672, 2000; Cutis 61:203–208, 1998; JAAD 19:854–858,
1988; BJD 68:385–394, 1956; resembles IgA pemphigus
JAAD 43:546–549, 2000; Cutis 61:225–226, 1998
Sybert keratoderma – autosomal dominant; palmoplantar
erythema with transgrediens distribution, intertriginous
hyperkeratosis, pseudo-ainhum with spontaneous amputations
JAAD 18:75–86, 1988
Terra firme
Transient neonatal pustular melanosis – diaper area 
Ghatan
p.108, 2002, Second Edition

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